Rare case of iridocorneal endothelial syndrome with secondary glaucoma

A rare case of 40 years old female, came with complaints pain and blurring vision in the left eye for past week. The patient had a diminution since birth her eye. On examination was found to be 6/60 not improving pinhole, also defective color 20/25. right-eye normal. showed significant corneal edema, moderate anterior chamber depth, iris features Corectopia, Pseudopolycoria, atrophy. Pressures were 30mm hg eye, gonioscopy revealed high peripheral synechiae extending anteriorly above Schwalbe’s line. Left fundoscopy done it increased CDR 0.8 0.9 following which visual field analysis done, inferior defect. started on e/d timolol hypertonic saline reviewed after week showing reduced pressures 22mmg edema pain. Diagnosis iridocorneal endothelial syndrome-essential atrophy type secondary glaucoma made now is being followed up regularly. An syndrome group disorders three clinical variants as Chandler syndrome, Essential atrophy, Cogan Reese syndrome. Pathology presence abnormal cells, behave epithelial able proliferate migrate. frequently associated glaucoma.